Primary congenital glaucoma (PCG) is a rare, vision-impairing disease with an estimated incidence of 1 in 5000 to 1 in 10,000 live births in Western countries [1]. The primary pathophysiology of PCG involves abnormalities in the trabecular meshwork and anterior chamber angle, leading to elevated intraocular pressure (IOP). In patients with PCG, characteristic ocular findings include increased axial length, enlarged corneal diameter, thinning of the anterior sclera and iris, and a normal fundus appearance except for glaucomatous optic atrophy [2].

Increased axial length in eyes with PCG is associated with an increased prevalence of peripheral retinal degeneration, as demonstrated by recent studies [3]. The aforementioned features of PCG contribute to an increased susceptibility to retinal detachment (RD) in affected individuals [4]. Delayed diagnosis of RD in children with PCG is often attributed to their limited vision and potential hindrance to retinal evaluation due to corneal opacities. Additionally, pre-existing ocular comorbidities like amblyopia, corneal opacity, and glaucomatous optic atrophy can negatively impact the final visual outcomes of RD surgery in these patients [5].

The literature on preoperative features and surgical outcomes of RD in patients with PCG remains limited, with only a few studies investigating this specific population [6]. This study aims to investigate the preoperative characteristics and long-term surgical outcomes of pediatric RD associated with PCG.