Sung H, et al. Global cancer statistics 2020: GLOBOCAN estimates of incidence and mortality worldwide for 36 cancers in 185 countries. CA Cancer J Clin. 2021;71(3):209–49.

Article  PubMed  Google Scholar 

Rahib L, Smith BD, Aizenberg R, Rosenzweig AB, Fleshman JM, Matrisian LM. Projecting cancer incidence and deaths to 2030: the unexpected burden of thyroid, liver, and pancreas cancers in the United States. Cancer Res. 2014;74(11):2913–21.

Article  CAS  PubMed  Google Scholar 

Chaudhary P. Acinar Cell Carcinoma of the Pancreas: A Literature Review and Update. Indian J Surg. 2015;77(3):226–31.

Article  PubMed  Google Scholar 

Calimano-Ramirez LF, et al. Pancreatic acinar cell carcinoma: A comprehensive review. World J Gastroenterol. 2022;28(40):5827–44.

Article  CAS  PubMed  PubMed Central  Google Scholar 

Yonkus JA, et al. A national database analysis of acinar cell carcinoma of the pancreas, a histologically, epidemiologically, and biologically distinct entity increasing in incidence. Ann Pancreat Cancer. 2021;4:3–3.

Article  Google Scholar 

Thompson ED, Wood LD. Pancreatic Neoplasms With Acinar Differentiation: A Review of Pathologic and Molecular Features. Arch Pathol Lab Med. 2020;144(7):808–15.

Article  CAS  PubMed  Google Scholar 

Duorui N, et al. The contemporary trend in worsening prognosis of pancreatic acinar cell carcinoma: A population-based study. PLoS ONE. 2020;15(12):e0243164.

Article  PubMed  PubMed Central  Google Scholar 

Kayahara M, et al. Pancreatic acinar cell carcinoma with extension into the main pancreatic duct: a case report. Surg Case Rep. 2021;7(1):90.

Article  PubMed  PubMed Central  Google Scholar 

Qu Q, Xin Y, Xu Y, Yuan Y, Deng K. Imaging and Clinicopathological Features of Acinar Cell Carcinoma. Front Oncol. 2022;12:888679.

Article  CAS  PubMed  PubMed Central  Google Scholar 

“SEER*Stat Databases: SEER November 2022 Submission,” Surveillance, Epidemiology and End Results. [Online]. Available: https://seer.cancer.gov/data-software/documentation/seerstat/nov2022/.

Petrova E, et al. Survival outcome and prognostic factors for pancreatic acinar cell carcinoma: retrospective analysis from the German cancer registry group. Cancers. 2021;13(23):6121. https://doi.org/10.3390/cancers13236121.

Article  PubMed  PubMed Central  Google Scholar 

He C, Zhang Y, Cai Z, Duan F, Lin X, Li S. Nomogram to predict cancer-specific survival in patients with pancreatic acinar cell carcinoma: A competing risk analysis. J Cancer. 2018;9(22):4117–27.

Article  CAS  PubMed  PubMed Central  Google Scholar 

Wisnoski NC, Townsend CM Jr, Nealon WH, Freeman JL, Riall TS. 672 patients with acinar cell carcinoma of the pancreas: a population-based comparison to pancreatic adenocarcinoma. Surgery. 2008;144(2):141–8.

Article  PubMed  Google Scholar 

Holen KD, et al. Clinical characteristics and outcomes from an institutional series of acinar cell carcinoma of the pancreas and related tumors. J Clin Oncol. 2002;20(24):4673–8.

Article  PubMed  Google Scholar 

Butturini G, Pisano M, Scarpa A, D’Onofrio M, Auriemma A, Bassi C. Aggressive approach to acinar cell carcinoma of the pancreas: a single-institution experience and a literature review. Langenbecks Arch Surg. 2011;396(3):363–9.

Article  PubMed  Google Scholar 

Lowery MA, et al. Acinar cell carcinoma of the pancreas: new genetic and treatment insights into a rare malignancy. Oncologist. 2011;16(12):1714–20.

Article  PubMed  PubMed Central  Google Scholar 

Schmidt CM, Matos JM, Bentrem DJ, Talamonti MS, Lillemoe KD, Bilimoria KY. Acinar cell carcinoma of the pancreas in the United States: prognostic factors and comparison to ductal adenocarcinoma. J Gastrointest Surg. 2008;12(12):2078–86.

Article  PubMed  Google Scholar 

Cananzi FCM, et al. ‘Chronic’ metastatic pancreatic acinar cell carcinoma. Pancreatology. 2013;13(5):549–52.

Article  PubMed  Google Scholar 

Sridharan V, et al. Pancreatic acinar cell carcinoma: a multi-center series on clinical characteristics and treatment outcomes. Pancreatology. 2021;21(6):1119–26. https://doi.org/10.1016/j.pan.2021.05.011.

Article  CAS  Google Scholar 

Yoo C, et al. Efficacy of chemotherapy in patients with unresectable or metastatic pancreatic acinar cell carcinoma: potentially improved efficacy with oxaliplatin-containing regimen. Cancer Res Treat. 2017;49(3):759–65.

Article  CAS  PubMed  Google Scholar 

Glazer ES, et al. Systematic review and case series report of acinar cell carcinoma of the pancreas. Cancer Control. 2016;23(4):446–54.

Article  PubMed  Google Scholar 

Al-Hader A, Al-Rohil RN, Han H, Von Hoff D. Pancreatic acinar cell carcinoma: A review on molecular profiling of patient tumors. World J Gastroenterol. 2017;23(45):7945–51.

Article  CAS  PubMed  PubMed Central  Google Scholar 

Callata-Carhuapoma HR, et al. Pancreatic acinar cell carcinoma with bilateral ovarian metastases, panniculitis and polyarthritis treated with FOLFIRINOX chemotherapy regimen. A case report and review of the literature. Pancreatology. 2015;15(4):440–4.

Article  PubMed  Google Scholar 

Yoshihiro T, et al. Pancreatic acinar cell carcinoma presenting with panniculitis, successfully treated with FOLFIRINOX: A case report. Mol Clin Oncol. 2017;6(6):866–70.

Article  PubMed  PubMed Central  Google Scholar 

Qin L, Shen J, Yang Y, Zou Z. Rapid response to the combination of lenvatinib and sintilimab in a pancreatic acinar cell carcinoma patient with elevated alpha-fetoprotein: a case report. Front Oncol. 2021;11:692480.

Article  PubMed  PubMed Central  Google Scholar 

“Olaparib in Subjects With Advanced Pancreatic Acinar Cell Carcinoma,” Clinicaltrials.gov identifier: NCT05286827, 22-Jan-2024. [Online]. Available: https://www.clinicaltrials.gov/study/NCT05286827?term=NCT05286827&rank=1&tab=table. Accessed 16 Mar 2024.

Jäkel C, et al. Genome-wide genetic and epigenetic analyses of pancreatic acinar cell carcinomas reveal aberrations in genome stability. Nat Commun. 2017;8(1):1323.

Article  PubMed  PubMed Central  Google Scholar 

Kim S, et al. The basic helix-loop-helix transcription factor E47 reprograms human pancreatic cancer cells to a quiescent acinar state with reduced tumorigenic potential. Pancreas. 2015;44(5):718–27.

Article  CAS  PubMed  PubMed Central  Google Scholar 

Kryklyva V, et al. Pancreatic acinar cell carcinoma is associated with BRCA2 germline mutations: a case report and literature review. Cancer Biol Ther. 2019;20(7):949–55.

Article  CAS  PubMed  PubMed Central  Google Scholar 

Gupta M, et al. Targeting the NTRK Fusion Gene in Pancreatic Acinar Cell Carcinoma: A Case Report and Review of the Literature. J Natl Compr Canc Netw. 2021;19(1):10–5.

Article  PubMed  PubMed Central  Google Scholar