Cottin V, Si-Mohamed S, Diesler R, Bonniaud P, Valenzuela C. Pleuroparenchymal fibroelastosis. Curr Opin Pulm Med. 2022;28:432–40.

Article  CAS  PubMed  Google Scholar 

Lee E, Chen-Yost H, Wang JM, Agarwal PP. Pleuroparenchymal fibroelastosis. Semin Roentgenol. 2026;61:150951.

Article  PubMed  Google Scholar 

Watanabe K. Pleuroparenchymal fibroelastosis: Its clinical characteristics. Curr Respir Med Rev. 2013;9:229–37.

Article  CAS  Google Scholar 

Nakamura Y, Mori K, Enomoto Y, Kono M, Sumikawa H, Johkoh T, et al. Prognostic and clinical value of cluster analysis in idiopathic pleuroparenchymal fibroelastosis phenotypes. J Clin Med. 2021;10:1498.

Article  PubMed  PubMed Central  Google Scholar 

Baqir M, LeMahieu AM, Hartman TE, Farah WH, Yi EE, Ryu JH. Pleuroparenchymal fibroelastosis: review of 81 cases. Expert Rev Respir Med. 2026;20:217–26.

Article  CAS  PubMed  Google Scholar 

Marathe PH, Santibanez V, Meyers PA, Padilla ML, Friedman DN. Pleuroparenchymal fibroelastosis as a late complication of childhood cancer therapy: A case series. Pediatr Blood Cancer. 2024;71:e31004.

Article  CAS  PubMed  Google Scholar 

Egashira A, Yoneshima Y, Mizusaki S, Tsuneoka Y, Tsubouchi K, Okamoto I. Pleuroparenchymal fibroelastosis secondary to autologous peripheral blood stem cell transplantation: A case report. Respir Med Case Rep. 2023;43:101845.

PubMed  PubMed Central  Google Scholar 

Oh S-L, Lee JW, Yoo S-Y, Kim JH, Kim YJ, Han J, et al. Pleuroparenchymal fibroelastosis after hematopoietic stem cell transplantation in children: a propensity score-matched analysis. Eur Radiol. 2023;33:2266–76.

Article  CAS  PubMed  Google Scholar 

Otth M, Kasteler R, Mulder RL, Agrusa J, Armenian SH, Barnea D, et al. Recommendations for surveillance of pulmonary dysfunction among childhood, adolescent, and young adult cancer survivors: a report from the International Late Effects of Childhood Cancer Guideline Harmonization Group. EClinicalMedicine. 2024;69:102487.

Article  PubMed  PubMed Central  Google Scholar 

Egashira R, Yamaguchi K, Kondo T, Nakazono T, Fukui S, Irie H. Pleuroparenchymal fibroelastosis (PPFE)-like finding on CT in daily practice: prevalence and serial changes. Eur J Radiol Open. 2020;7:100296.

Article  PubMed  PubMed Central  Google Scholar 

Becker CD, Gil J, Padilla ML. Idiopathic pleuroparenchymal fibroelastosis: an unrecognized or misdiagnosed entity? Mod Pathol. 2008;21:784–7.

Article  CAS  PubMed  Google Scholar 

Yamakawa H, Oda T, Sugino K, Hirama T, Komatsu M, Katano T, et al. Proposed clinical algorithm for pleuroparenchymal fibroelastosis (PPFE). J Clin Med. 2024;13:3675.

Article  CAS  PubMed  PubMed Central  Google Scholar 

DeVine A, Landier W, Hudson MM, Constine LS, Bhatia S, Armenian SH, et al. The Children’s Oncology Group long-Term Follow-Up Guidelines for survivors of childhood, adolescent, and Young Adult Cancers: A review. JAMA Oncol. 2025;11:544–53.

Article  PubMed  PubMed Central  Google Scholar 

Suzuki Y, Fukada A, Mori K, Kono M, Hasegawa H, Hashimoto D, et al. Assessment of malnutrition-related risk in patients with idiopathic pleuroparenchymal fibroelastosis. ERJ Open Res. 2023;9:00749–2022.

Article  PubMed  PubMed Central  Google Scholar 

Iwasaki K, Watanabe S, Kase K, Ohkura N, Saeki K, Tambo Y, et al. Prognostic value of coexisting conditions and complications in pleuroparenchymal fibroelastosis: a single-center retrospective study. Sarcoidosis Vasc Diffuse Lung Dis. 2024;41:e2024014.

PubMed  PubMed Central  Google Scholar 

Enomoto Y, Nakamura Y, Satake Y, Sumikawa H, Johkoh T, Colby TV, et al. Clinical diagnosis of idiopathic pleuroparenchymal fibroelastosis: a retrospective multicenter study. Respir Med. 2017;133:1–5.

Article  PubMed  Google Scholar 

Ishii H, Kinoshita Y, Kushima H, Nagata N, Watanabe K. The similarities and differences between pleuroparenchymal fibroelastosis and idiopathic pulmonary fibrosis. Chron Respir Dis. 2019;16:1479973119867945.

Article  PubMed  PubMed Central  Google Scholar 

Yamamoto Y, Tsujino K, Kuge T, Okabe F, Kawasaki T, Matsuki T, et al. Pleuroparenchymal fibroelastosis in Mycobacterium avium complex pulmonary disease: clinical characteristics and prognostic impact. ERJ Open Res. 2021;7:00765–2020.

Article  PubMed  PubMed Central  Google Scholar 

Muto Y, Sekine A, Hagiwara E, Komatsu S, Baba T, Oda T, et al. Clinical characteristics of pulmonary hypertension in patients with pleuroparenchymal fibroelastosis. Respir Investig. 2022;60:543–50.

Article  PubMed  Google Scholar 

Cueto-Robledo G, Guerrero-Velazquez J-F, Roldan-Valadez E, Graniel-Palafox L-E, Cervantes-Naranjo F-D, Cueto-Romero H-D, et al. Pulmonary hypertension or pulmonary arterial hypertension in idiopathic pleuroparenchymal fibroelastosis: an updated comprehensive review. Curr Probl Cardiol. 2022;47:101368.

Article  PubMed  Google Scholar 

Watanabe K, Ishii H, Kiyomi F, Terasaki Y, Hebisawa A, Kawabata Y, et al. Criteria for the diagnosis of idiopathic pleuroparenchymal fibroelastosis: A proposal. Respir Investig. 2019;57:312–20.

Article  PubMed  Google Scholar 

Fukada A, Suzuki Y, Mori K, Kono M, Hasegawa H, Hashimoto D, et al. Idiopathic pleuroparenchymal fibroelastosis: three-dimensional computed tomography assessment of upper-lobe lung volume. Eur Respir J. 2022;60:2200637.

Article  CAS  PubMed  Google Scholar 

Konoeda C, Toyokawa G, Yamaguchi M, Yamaya T, Akamine T, Kawashima M, et al. Impact of flat chest on waitlist mortality in adult patients with pleuroparenchymal fibroelastosis listed for lung transplantation. JHLT Open. 2026;12:100509.

Article  PubMed  PubMed Central  Google Scholar 

Gudmundsson E, Zhao A, Mogulkoc N, van Beek F, Goos T, Brereton CJ, et al. Delineating associations of progressive pleuroparenchymal fibroelastosis in patients with pulmonary fibrosis. ERJ Open Res. 2023;9:00637–2022.

Article  PubMed  PubMed Central  Google Scholar 

Oda T, Sekine A, Tabata E, Iwasawa T, Takemura T, Ogura T. Comparison of clinical characteristics and outcomes between idiopathic and secondary pleuroparenchymal fibroelastosis. J Clin Med. 2021;10:846.

Article  PubMed  PubMed Central  Google Scholar 

Shioya M, Otsuka M, Yamada G, Umeda Y, Ikeda K, Nishikiori H, et al. Poorer prognosis of idiopathic pleuroparenchymal fibroelastosis compared with idiopathic pulmonary fibrosis in advanced stage. Can Respir J. 2018;2018:6043053.

PubMed  PubMed Central  Google Scholar 

Gudmundsson E, Zhao A, Mogulkoc N, Stewart I, Jones MG, Van Moorsel CHM, et al. Pleuroparenchymal fibroelastosis in idiopathic pulmonary fibrosis: Survival analysis using visual and computer-based computed tomography assessment. EClinicalMedicine. 2021;38:101009.

Article  PubMed  PubMed Central  Google Scholar 

Suzuki Y, Kono M, Hasegawa H, Hashimoto D, Yokomura K, Inoue Y, et al. Prognostic value of computed tomography assessment of normal lung volume in upper lobe in idiopathic pleuroparenchymal fibroelastosis. ERJ Open Res. 2025;11(3):00687–2024.

Article  PubMed  PubMed Central  Google Scholar 

Matsunashi A, Maetani T, Handa T, Ikezoe K, Uozumi R, Tanabe N, et al. Comprehensive quantitation of bronchial and lung parenchymal lesions in idiopathic pleuroparenchymal fibroelastosis. Respir Med. 2025;249:108468.

Article  PubMed  Google Scholar 

Suzuki Y. Idiopathic pleuroparenchymal fibroelastosis: A review of the previous literature and current knowledge. Respir Investig. 2025;63:127–37.

Article  PubMed  Google Scholar 

Mariani F, Gatti B, Rocca A, Bonifazi F, Cavazza A, Fanti S, et al. Pleuroparenchymal fibroelastosis: the prevalence of secondary forms in hematopoietic stem cell and lung transplantation recipients. Diagn Interv Radiol. 2016;22:400–6.

Article  PubMed  PubMed Central  Google Scholar 

Sarı A, Önder Ö, Armağan B, Bölek EÇ, Farisoğulları B, Bilgin E, et al. Pleuroparenchymal fibroelastosis in systemic sclerosis-associated interstitial lung disease. Turk J Med Sci. 2022;52:83–8.